Table 1 Clinical and laboratory finding of the patients in this study

Family history available

No

Yes

No

Age at the time of the study

4 years

21 months

16 months

Age at onset

3 years

17 months

16 month

Fever

Yes

Yes

Yes

Hepatomegaly

4 cm

5 cm

2.5 cm

Splenomegaly

2 cm

3 cm

1 cm

White blood cells (×10⁹/L)

11.6

6.36

3.03

Neutrophils (×10⁹/L)

1.61

3.915

0.56

Hemoglobin (g/dL)

8.1

9.6

7.5

Platelets (×10⁹/L)

95

56

30

LDH (IU/L)

449

1,693

1,698

AST (IU/L)

88

122

453

ALT (IU/L)

31

25

255

Ferritin (μg/L)

1,276

26,282

11,129

sIL-2R (U/mL)

3,162

2,880

14,334

IgG (mg/dL)

1,821

806

423

IgA (mg/dL)

302

124

32

IgM (mg/dL)

1,843

40

18

Whole blood EBV-DNA (copies/mL)

140,000

5,700

1,400,000